Welcome to International Journal of Anatomy and Research

Type of Article: Case Report

Year: 2016 | Volume 4 | Issue 3 | Page No. 2813-2816

Date of Publication: 30-09-2016

DOI: http://dx.doi.org/10.16965/ijar.2016.341

POLYMELIA ASSOCIATED WITH LIPOMYELOMENINGOCELE: A CASE REPORT

Rajendra Retnam K ¹, Dhanalakshmi V ², Flora Juanita E ³, Jeyanthi GnanaMuthu ⁴.

¹ Professor, Department of Neurosurgery, Govt. Thoothukudi Medical College, Thoothukudi, Tamilnadu, India.

² Assistant Professor, Department of Anatomy, Govt. Thoothukudi Medical College, Thoothukudi, Tamilnadu, India.

³ Associate Professor, Department of Radiology, Govt. Thoothukudi Medical College, Thoothukudi, Tamilnadu, India.

⁴ Associate Professor, Department of Pathology, Govt. Thoothukudi Medical College, Thoothukudi, Tamilnadu, India. .

Address: Dhanalakshmi V, Assistant Professor, Department of Anatomy, Govt. Thoothukudi Medical College, Thoothukudi, Tamilnadu, India. Mobile: 9443671671
E-Mail: drlakshmidhana@gmail.com

ABSTRACT

Polymelia is a congenital defect involving limbs, in which the affected individual has more than the usual number of limbs. The supernumerary limb can be either shrunken or deformed and can be attached to various regions of the body. Supernumerary limb attached to a lipomyelomeningocele is very rarely reported and we report a case of 4 months old male baby born to parents of non- consanguineous marriage presented with supernumerary lower limb of length 9cm attached to lipomyelomeningocele at the lumbosacral region of size 18x13cm. Surgery was performed with untethering of the spinal cord, debulking of the lipoma and excision of the supernumerary limb. On histopathological examination lipomatous tissue was confirmed and on meticulous dissection of the supernumerary limb, it had bone exposed at one end and the other end had two digits of length 1.4 and 1cm. The limb had features of sole with partially developed plantar aponeurosis, muscles and blood vessels. Thigh and leg were not formed fully. These malformations can have multifactorial etiology and antenatal diagnosis can be done by ultrasonogram. Early surgical management can prevent neurological complications.
Key words: Polymelia, lipomyelomeningocele, supernumerary, congenital. 

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Rajendra Retnam K, Dhanalakshmi V, Flora Juanita E, Jeyanthi GnanaMuthu. POLYMELIA ASSOCIATED WITH LIPOMYELOMENINGOCELE: A CASE REPORT. Int J Anat Res 2016;4(3):2813-2816. DOI: 10.16965/ijar.2016.341